Antenatal diagnosis of total arrhinia based on ultrasonographic findings has been described. Arhinia per se is not life threatening but the immediate and long-term outcomes of the neonate are dependent on associated anomalies. The afflicted neonate may need emergency resuscitation due to respiratory distress. In this case there was laryngeal stenosis which was the probable cause of death. The technique and timing of the reparative procedures of the nasal structures is also a medical controversy. Parental counselling is important. A multidisciplinary team effort is required for best neonatal results.
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